Resident Physician, Pediatrics University of Florida Jacksonville - Jacksonville, FL Jacksonville, Florida, United States
Background: Anomalous aortic origin of a coronary artery is the second most common cause of sudden cardiac death (SCD) in young athletes in the US. Anomalous aortic origin of the right coronary artery from the left sinus of Valsalva (AAORCA) is 5 times more common that anomalous aortic origin of the left from the right sinus (AAOLCA). Given the higher risk of SCD, diagnosis of AAOLCA leads to recommending surgical correction. In AAORCA, the conventional approach recommends surgical correction only when there are ischemic symptoms, or high-risk anatomic features. However, not all AAORCA patients have symptoms or positive stress tests before SCD, leading centers to offer correction to all patients. The risk of surgical intervention, however, is incompletely understood. Thus, it is important to analyze post-intervention complications of AAORCA repair to further assess the risk of surgical intervention, as it may aid with future determinations of the appropriate guidelines for surgical intervention of AAORCA. Objective: Primary: Examine indications prompting diagnosis, investigative modalities used, surgical techniques, short and medium-term follow-up following surgery. Secondary: Examine risk of follow-up surgical or catheter-based intervention Design/Methods: IRB-approved retrospective chart review of patients less than 18 years of age who underwent surgical correction of AAORCA at Wolfson’s Children’s Hospital between 07/01/2012 and 12/31/2022, identified from the congenital cardiac surgical program database. Following data will be collected from the EMR and de-identified: demographics, symptoms, cardiac testing results, coronary anatomy, surgical technique, follow-up. Continuous variables will be summarized by means, medians, and standard deviations; and categorial variables by frequencies and proportions. Primary and secondary endpoints will be analyzed according the characteristics of the AAORCA.
